| 원발성 가역적뇌혈관수축증후군에 의한 가역적후뇌병증 |
| 최윤호·조유나·고 원·류철형·김원주·최영철 |
| 연세대학교 의과대학 강남세브란스병원 신경과학교실 |
| Posterior Reversible Encephalopathy Syndrome Due to Primary Reversible Cerebral Vasoconstriction Syndrome |
| Yun Ho Choi, MD, Yu Na Cho, MD, Won Ko, MD, Chul Hyoung Lyoo, MD, PhD, Won-Joo Kim, MD, PhD and Young-Chul Choi, MD, PhD |
| Department of Neurology, Gangnam Severance Hospital, Yonsei University College of Medicine, Seoul, Korea |
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| ABSTRACT |
Background: Reversible cerebral vasoconstriction syndrome (RCVS) is an underdiagnosed disease characterized by severe headaches with or without seizures, focal neurological deficits, and constriction of cerebral arteries which resolves spontaneously in 1-3 months. Posterior reversible encephalopathy syndrome (PRES) is typically characterized by headache, altered mental functioning, seizures, and visual loss associated with imaging findings of bilateral subcortical and cortical edema with a predominantly posterior distribution.
Case Report: We present 49-year-old and 46-year-old females with thunderclap headache and seizure. MRI shows reversible cortical and subcortical lesions in both fronto-parieto-occipital lobes. And magnetic resonance angiography shows reversible multifocal luminal narrowing of distal cerebral vessels.
Conclusions: Primary RCVS may occur as a cause of PRES. We report two cases of non-hypertensive PRES with seizure due to primary RCVS presenting thunderclap headache. |
| Key Words:
Reversible cerebral vasoconstriction syndrome · Posterior reversible encephalopathy syndrome · Thunderclap headache |
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