Posterior Reversible Encephalopathy Syndrome Due to Primary Reversible Cerebral Vasoconstriction Syndrome
Yun Ho Choi, MD, Yu Na Cho, MD, Won Ko, MD, Chul Hyoung Lyoo, MD, PhD, Won-Joo Kim, MD, PhD and Young-Chul Choi, MD, PhD
Department of Neurology, Gangnam Severance Hospital, Yonsei University College of Medicine, Seoul, Korea
ABSTRACT
Background: Reversible cerebral vasoconstriction syndrome (RCVS) is an underdiagnosed disease characterized by severe headaches with or without seizures, focal neurological deficits, and constriction of cerebral arteries which resolves spontaneously in 1-3 months. Posterior reversible encephalopathy syndrome (PRES) is typically characterized by headache, altered mental functioning, seizures, and visual loss associated with imaging findings of bilateral subcortical and cortical edema with a predominantly posterior distribution. Case Report: We present 49-year-old and 46-year-old females with thunderclap headache and seizure. MRI shows reversible cortical and subcortical lesions in both fronto-parieto-occipital lobes. And magnetic resonance angiography shows reversible multifocal luminal narrowing of distal cerebral vessels. Conclusions: Primary RCVS may occur as a cause of PRES. We report two cases of non-hypertensive PRES with seizure due to primary RCVS presenting thunderclap headache.
PDF Links
Full text via DOI 
Download Citation 
CrossRef TDM
E-Mail 
